Management of Patient with Limb Girdle Muscular Dystrophy for ERCP and Regional Anaesthesia for Laparoscopic Cholecystectomy: Case Report

Vol 3 | Issue 1 | January-June 2022 | Page 27-30 | Shalini Saksena , Arnab Paul

DOI: 10.13107/ijra.2022.v03i01.051


Authors: Shalini Saksena [1], Arnab Paul [1]

[1] Department of Anaesthesia, PD Hinduja National Hospital & MRC, Mahim, Mumbai, Maharashtra, India.

Address of Correspondence:
Dr. Arnab Paul,
Department of Anaesthesia, PD Hinduja National Hospital & MRC, Mahim, Mumbai, Maharashtra, India.
E-mail: dr.arnabpaul88@gmail.com


Abstract


Limb-Girdle muscular dystrophies (LGMDs) are a clinically and genetically heterogeneous group of disorders characterized in general by predominantly limb-girdle weakness. It manifests as proximal muscle weakness involving the pelvic girdle and scapular girdle. We report the anaesthetic management of a patient who is a known case of limb-girdle muscular dystrophy, presented with cholecystitis to our institution. Patient underwent endoscopic retrograde cholangio pancreatography (ERCP) under total intravenous anaesthesia followed by laparoscopic cholecystectomy under spinal anaesthesia which were managed successfully.
Keywords: Muscular Dystrophies, Limb-Girdle, Malignant Hyperthermia, Anaesthesia


References


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10. Catani M, Guerricchio R, De Milito R, et al. ‘Low-pressure’ laparoscopic cholecystectomy in high-risk patients (ASA III and IV): our experience. Chir Ital 2004; 56:71–80.
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How to Cite this Article: Saksena S, Paul A | Management of Patient With Limb Girdle Muscular Dystrophy for ERCP and Regional Anaesthesia for Laparoscopic Cholecystectomy: Case Report | International Journal of Regional Anaesthesia | January-June 2022; 3(1): 27-30.

 


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