Spinal Anaesthesia for Inguinal Herniotomy in an Infant with Mucopolysaccharidosis type III with skeletal dwarfism: A Case Report

Vol 6 | Issue 2 | July-December 2025 | Page 00-00 | Sreyashi Naskar , K R Chandrakala , Soumya Nayak

DOI: https://doi.org/10.13107/ijra.2025.v06.i02.000

Open Access License: CC BY-NC 4.0

Copyright Statement: Copyright © 2025; The Author(s).

Submitted: 01-06-2025; Reviewed: 29-06-2025; Accepted: 13-11-2025; Published: 10-12-2025

Authors: Sreyashi Naskar [1], K R Chandrakala [1], Soumya Nayak [1]

[1] Department of Paediatric Anaesthesiology, Indira Gandhi Institute of Child Health, Bangalore, Karnataka, India.

Address of Correspondence

Dr. Sreyashi Naskar,
Department of Paediatric Anaesthesiology, Indira Gandhi Institute of Child Health, Bangalore, Karnataka. India
E-mail id: sreyashi.n@gmail.com

Abstract

Mucopolysaccharidosis (MPS) is an inherited lysosomal storage disorder where glycosaminoglycans accumulate in various connective tissues, resulting into a myriad of organ system abnormalities. One of the most challenging aspect of their anaesthesia management is airway control, as these are almost always deemed difficult airway subjects. Anaesthetising neonates or small infants with MPS proves to be an even more critical scenario due to their added airway and respiratory physiological characteristics. Conducting surgeries on such patients under sole regional/ neuraxial anaesthesia can be an extremely efficacious and safe approach, provided the difficulties in their neuraxial anatomy are kept in mind, and thereof, managed accordingly. However, sole neuraxial anaesthesia in small children with MPS is scantly reported in existing literature and hence needs further reporting and study.
Keywords: Mucopolysaccharidoses, Mucopolysaccharidosis III, Obstructive Sleep Apneas, Dwarfism, Airway management

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